Vine-like vessels in the eye

This fundus photograph of the right eye of a 4 year old girl shows abnormally dilated and vine-like retinal vessels (fig 1). Her best corrected visual acuity was 20/50 in the right eye and 20/20 in the left. She had no other symptoms of note. No abnormalities were detected on facial and brain magnetic resonance imaging but fluorescein angiography showed leakage from the temporal retinal vessel in the right eye. bmj;386/jul25_4/e078379/F1F1f1Fig 1The patient was diagnosed as having retinal racemose haemangioma (RRH), a non-hereditary congenital anatomical arteriovenous malformation that occurs only in the eye. RRH is characterised by dilated and tortuous retinal vessels extending from the disc to the retinal periphery. As many as 30% of patients with RRH might have a concurrent neurocutaneous syndrome with vascular abnormalities of the brain and face, known as Wyburn-Mason syndrome.1 Brain imaging is therefore necessary to exclude this condition.RRH remains stable in most patients,…
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